Xylulose is a ketopentose, a monosaccharide containing five carbon , and including a ketone functional group. It has the chemical formula . In nature, it occurs in both the L- and D-. 1-Deoxyxylulose is a precursor to via the DOXP pathway.
Pathology
L-Xylulose accumulates in the
urine in patients with
pentosuria, due to a deficiency in L-xylulose reductase. Since
L-xylulose is a reducing sugar like
D-glucose, pentosuria patients have been wrongly diagnosed in the past to be
diabetic.